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Go!
Schema
>
SimpleEntity
>
Entries
4aOH-BH4 [cytosol]
Show undefined attributes
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compartment
[Compartment:70101] cytosol
consumedByEvent
[Reaction:R-HSA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Homo sapiens
[Reaction:R-MMU-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Mus musculus
[Reaction:R-RNO-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Rattus norvegicus
[Reaction:R-CFA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Canis familiaris
[Reaction:R-BTA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Bos taurus
[Reaction:R-SSC-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Sus scrofa
[Reaction:R-DRE-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Danio rerio
[Reaction:R-XTR-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Xenopus tropicalis
[Reaction:R-GGA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Gallus gallus
[Reaction:R-DME-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Drosophila melanogaster
[Reaction:R-CEL-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Caenorhabditis elegans
[Reaction:R-DDI-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Dictyostelium discoideum
[Reaction:R-SPO-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Schizosaccharomyces pombe
[Reaction:R-SCE-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Saccharomyces cerevisiae
[Reaction:R-PFA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O - Plasmodium falciparum
dbId
71112
displayName
4aOH-BH4 [cytosol]
inDisease
false
literatureReference
[Book:71113] The Metabolic and Molecular Bases of Inherited Disease, 8th ed Scriver, CR Disorders of tetrahydrobiopterin and related biogenic amines 0079130356
maxDepth
1
modified
[InstanceEdit:9929230] D'Eustachio, Peter, 2024年11月22日
name
4aOH-BH4
4a-hydroxytetrahydrobiopterin
producedByEvent
[Reaction:R-CEL-209823] Tyrosine is hydroxylated to dopa - Caenorhabditis elegans
[Reaction:R-DME-209823] Tyrosine is hydroxylated to dopa - Drosophila melanogaster
[Reaction:R-GGA-209823] Tyrosine is hydroxylated to dopa - Gallus gallus
[Reaction:R-XTR-209823] Tyrosine is hydroxylated to dopa - Xenopus tropicalis
[Reaction:R-HSA-209828] Tryptophan is hydroxylated - Homo sapiens
[Reaction:R-MMU-209828] Tryptophan is hydroxylated - Mus musculus
[Reaction:R-RNO-209828] Tryptophan is hydroxylated - Rattus norvegicus
[Reaction:R-CFA-209828] Tryptophan is hydroxylated - Canis familiaris
[Reaction:R-BTA-209828] Tryptophan is hydroxylated - Bos taurus
[Reaction:R-SSC-209828] Tryptophan is hydroxylated - Sus scrofa
[Reaction:R-DRE-209828] Tryptophan is hydroxylated - Danio rerio
[Reaction:R-GGA-209828] Tryptophan is hydroxylated - Gallus gallus
[Reaction:R-DME-209828] Tryptophan is hydroxylated - Drosophila melanogaster
[Reaction:R-CEL-209828] Tryptophan is hydroxylated - Caenorhabditis elegans
[Reaction:R-DDI-209828] Tryptophan is hydroxylated - Dictyostelium discoideum
[Reaction:R-HSA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Homo sapiens
[Reaction:R-MMU-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Mus musculus
[Reaction:R-RNO-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Rattus norvegicus
[Reaction:R-CFA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Canis familiaris
[Reaction:R-BTA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Bos taurus
[Reaction:R-SSC-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Sus scrofa
[Reaction:R-DRE-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Danio rerio
[Reaction:R-XTR-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Xenopus tropicalis
[Reaction:R-GGA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Gallus gallus
[Reaction:R-DME-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Drosophila melanogaster
[Reaction:R-CEL-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Caenorhabditis elegans
[Reaction:R-DDI-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr - Dictyostelium discoideum
[Reaction:R-DDI-209823] Tyrosine is hydroxylated to dopa - Dictyostelium discoideum
[Reaction:R-HSA-209823] Tyrosine is hydroxylated to dopa - Homo sapiens
[Reaction:R-MMU-209823] Tyrosine is hydroxylated to dopa - Mus musculus
[Reaction:R-RNO-209823] Tyrosine is hydroxylated to dopa - Rattus norvegicus
[Reaction:R-CFA-209823] Tyrosine is hydroxylated to dopa - Canis familiaris
[Reaction:R-BTA-209823] Tyrosine is hydroxylated to dopa - Bos taurus
[Reaction:R-SSC-209823] Tyrosine is hydroxylated to dopa - Sus scrofa
[Reaction:R-DRE-209823] Tyrosine is hydroxylated to dopa - Danio rerio
referenceEntity
[ReferenceMolecule:chebi:15642] 4a-hydroxy-L-erythro-5,6,7,8-tetrahydrobiopterin [ChEBI:15642]
referenceType
ReferenceMolecule
schemaClass
SimpleEntity
stId
R-ALL-71112
updateTrackers
[UpdateTracker:9940040] Update Tracker - [SimpleEntity:71112] 4aOH-BH4 [cytosol] - v92:[add_removeReferenceEntity]
[UpdateTracker:9889785] Update Tracker - [SimpleEntity:71112] 4aOH-BH4 [cytosol] - v52:[addName]
Referrals
(input)
[Reaction:R-HSA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-MMU-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-RNO-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-CFA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-BTA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-SSC-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-DRE-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-XTR-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-GGA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-DME-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-CEL-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-DDI-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-SPO-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-SCE-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
[Reaction:R-PFA-71146] 4a-hydroxytetrahydrobiopterin => q-dihydrobiopterin + H2O
(output)
[Reaction:R-CEL-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-DME-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-GGA-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-XTR-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-HSA-209828] Tryptophan is hydroxylated
[Reaction:R-MMU-209828] Tryptophan is hydroxylated
[Reaction:R-RNO-209828] Tryptophan is hydroxylated
[Reaction:R-CFA-209828] Tryptophan is hydroxylated
[Reaction:R-BTA-209828] Tryptophan is hydroxylated
[Reaction:R-SSC-209828] Tryptophan is hydroxylated
[Reaction:R-DRE-209828] Tryptophan is hydroxylated
[Reaction:R-GGA-209828] Tryptophan is hydroxylated
[Reaction:R-DME-209828] Tryptophan is hydroxylated
[Reaction:R-CEL-209828] Tryptophan is hydroxylated
[Reaction:R-DDI-209828] Tryptophan is hydroxylated
[Reaction:R-HSA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-MMU-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-RNO-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-CFA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-BTA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-SSC-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-DRE-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-XTR-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-GGA-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-DME-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-CEL-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-DDI-71118] PAH:Fe2+ tetramer hydroxylates L-Phe to L-Tyr
[Reaction:R-DDI-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-HSA-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-MMU-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-RNO-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-CFA-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-BTA-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-SSC-209823] Tyrosine is hydroxylated to dopa
[Reaction:R-DRE-209823] Tyrosine is hydroxylated to dopa
(updatedInstance)
[UpdateTracker:9940040] Update Tracker - [SimpleEntity:71112] 4aOH-BH4 [cytosol] - v92:[add_removeReferenceEntity]
[UpdateTracker:9889785] Update Tracker - [SimpleEntity:71112] 4aOH-BH4 [cytosol] - v52:[addName]
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