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Schema
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Pathway
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Entries
Urea cycle
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authored
[InstanceEdit:73677] D'Eustachio, P, 2003年06月24日 00:00:00
dbId
70635
deleted
[Deleted:507853] Deletion of instance: 70693
displayName
Urea cycle
doi
10.3180/REACT_847.1
edited
[InstanceEdit:165080] D'Eustachio, P, 0000-00-00 00:00:00
eventOf
[Pathway:R-HSA-71291] Metabolism of amino acids and derivatives - Homo sapiens
goBiologicalProcess
[GO_BiologicalProcess:20612] urea cycle
hasDiagram
true
hasEHLD
false
hasEvent
[Reaction:R-HSA-70542] glutamate + acetyl CoA => N-acetyl glutamate + CoA - Homo sapiens
[Reaction:R-HSA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Homo sapiens
[Reaction:R-HSA-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Homo sapiens
[Reaction:R-HSA-70577] ASS1 tetramer:NMRAL1 dimer:NADPH transforms L-Asp and L-Cit to ARSUA - Homo sapiens
[Reaction:R-HSA-70573] argininosuccinate <=> fumarate + arginine - Homo sapiens
[Reaction:R-HSA-70569] arginine + H2O => ornithine + urea [ARG1] - Homo sapiens
[Reaction:R-HSA-452036] arginine + H2O => ornithine + urea [ARG2] - Homo sapiens
[Reaction:R-HSA-70634] ornithine (cytosolic) + citrulline (mitochondrial) => ornithine (mitochondrial) + citrulline (cytosolic) - Homo sapiens
isInDisease
false
isInferred
false
lastUpdatedDate
2016年03月24日
literatureReference
[Book:70549] Urea cycle enzymes 0079130356 Scriver, CR The Metabolic and Molecular Bases of Inherited Disease, 8th ed
maxDepth
2
modified
[InstanceEdit:11064438] Weiser, Joel, 2025年08月28日
name
Urea cycle
Urea synthesis
orthologousEvent
[Pathway:R-SSC-70635] Urea cycle - Sus scrofa
[Pathway:R-PFA-70635] Urea cycle - Plasmodium falciparum
[Pathway:R-SCE-70635] Urea cycle - Saccharomyces cerevisiae
[Pathway:R-SPO-70635] Urea cycle - Schizosaccharomyces pombe
[Pathway:R-DDI-70635] Urea cycle - Dictyostelium discoideum
[Pathway:R-CEL-70635] Urea cycle - Caenorhabditis elegans
[Pathway:R-DME-70635] Urea cycle - Drosophila melanogaster
[Pathway:R-GGA-70635] Urea cycle - Gallus gallus
[Pathway:R-XTR-70635] Urea cycle - Xenopus tropicalis
[Pathway:R-DRE-70635] Urea cycle - Danio rerio
[Pathway:R-BTA-70635] Urea cycle - Bos taurus
[Pathway:R-CFA-70635] Urea cycle - Canis familiaris
[Pathway:R-RNO-70635] Urea cycle - Rattus norvegicus
[Pathway:R-MMU-70635] Urea cycle - Mus musculus
previousReviewStatus
[ReviewStatus:9821384] two stars
releaseDate
2003年03月31日
reviewStatus
[ReviewStatus:9821382] five stars
revised
[InstanceEdit:452018] D'Eustachio, P, 2010年01月14日
schemaClass
Pathway
species
[Species:48887] Homo sapiens
stId
R-HSA-70635
summation
[Summation:70637] The urea cycle yields urea, the major form in which excess n...
updateTrackers
[UpdateTracker:9783547] Update Tracker - [Pathway:70635] Urea cycle - v56:[updateContainedRLE]
[UpdateTracker:9791746] Update Tracker - [Pathway:70635] Urea cycle - v26:[updateContainedRLE]
[UpdateTracker:9789644] Update Tracker - [Pathway:70635] Urea cycle - v37:[updateContainedRLE]
[UpdateTracker:9790879] Update Tracker - [Pathway:70635] Urea cycle - v32:[addHasEvent, modifyText, updateContainedRLE]
Referrals
(updatedInstance)
[UpdateTracker:9783547] Update Tracker - [Pathway:70635] Urea cycle - v56:[updateContainedRLE]
[UpdateTracker:9791746] Update Tracker - [Pathway:70635] Urea cycle - v26:[updateContainedRLE]
[UpdateTracker:9789644] Update Tracker - [Pathway:70635] Urea cycle - v37:[updateContainedRLE]
[UpdateTracker:9790879] Update Tracker - [Pathway:70635] Urea cycle - v32:[addHasEvent, modifyText, updateContainedRLE]
(replacementInstances)
[Deleted:507853] Deletion of instance: 70693
(hasEvent)
[Pathway:R-HSA-71291] Metabolism of amino acids and derivatives
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