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Schema
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Reaction
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Entries
carbamoyl phosphate + ornithine => citrulline + orthophosphate
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authored
[InstanceEdit:73677] D'Eustachio, P, 2003年06月24日 00:00:00
catalystActivity
[CatalystActivity:70559] ornithine carbamoyltransferase activity of OTC trimer [mitochondrial matrix]
catalystActivityReference
[CatalystActivityReference:9643158] ornithine carbamoyltransferase activity of OTC trimer [mitochondrial matrix] Structure and expression of a complementary DNA for the nuclear coded precursor of human mitochondrial ornithine transcarbamylase
category
transition
compartment
[Compartment:5460] mitochondrial matrix
crossReference
[DatabaseIdentifier:12610658] Rhea:19514
dbId
70560
displayName
carbamoyl phosphate + ornithine => citrulline + orthophosphate
edited
[InstanceEdit:73677] D'Eustachio, P, 2003年06月24日 00:00:00
eventOf
[Pathway:R-HSA-70635] Urea cycle - Homo sapiens
followingEvent
[Reaction:R-HSA-70634] ornithine (cytosolic) + citrulline (mitochondrial) => ornithine (mitochondrial) + citrulline (cytosolic) - Homo sapiens
input
[SimpleEntity:R-ALL-29676] CAP [mitochondrial matrix]
[SimpleEntity:R-ALL-113585] L-Orn [mitochondrial matrix]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:71418] Structure and expression of a complementary DNA for the nuclear coded precursor of human mitochondrial ornithine transcarbamylase
[LiteratureReference:452023] Human ornithine transcarbamylase: crystallographic insights into substrate recognition and conformational changes
maxDepth
1
modified
[InstanceEdit:11033291] Weiser, Joel, 2025年08月28日
name
carbamoyl phosphate + ornithine => citrulline + orthophosphate
orthologousEvent
[Reaction:R-MMU-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Mus musculus
[Reaction:R-SCE-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Saccharomyces cerevisiae
[Reaction:R-SPO-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Schizosaccharomyces pombe
[Reaction:R-XTR-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Xenopus tropicalis
[Reaction:R-RNO-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Rattus norvegicus
[Reaction:R-GGA-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Gallus gallus
[Reaction:R-SSC-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Sus scrofa
[Reaction:R-BTA-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Bos taurus
[Reaction:R-CFA-70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - Canis familiaris
output
[SimpleEntity:R-ALL-113567] L-Cit [mitochondrial matrix]
[SimpleEntity:R-ALL-113548] Pi [mitochondrial matrix]
precedingEvent
[Reaction:R-HSA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Homo sapiens
[Reaction:R-HSA-70634] ornithine (cytosolic) + citrulline (mitochondrial) => ornithine (mitochondrial) + citrulline (cytosolic) - Homo sapiens
[Reaction:R-HSA-70666] glutamate + L-glutamate gamma-semialdehyde <=> ornithine + alpha-ketoglutarate [OAT] - Homo sapiens
releaseDate
2004年07月06日
reviewStatus
[ReviewStatus:9821382] five stars
revised
[InstanceEdit:452018] D'Eustachio, P, 2010年01月14日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-70560
summation
[Summation:178528] Mitochondrial ornithine transcarbamoylase (OTC) catalyzes th...
updateTrackers
[UpdateTracker:9791127] Update Tracker - [Reaction:70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - v32:[addLiteratureReference, modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9791127] Update Tracker - [Reaction:70560] carbamoyl phosphate + ornithine => citrulline + orthophosphate - v32:[addLiteratureReference, modifyText]
(hasEvent)
[Pathway:R-HSA-70635] Urea cycle
(precedingEvent)
[Reaction:R-HSA-70634] ornithine (cytosolic) + citrulline (mitochondrial) => ornithine (mitochondrial) + citrulline (cytosolic)
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