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Reaction
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Entries
CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1
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authored
[InstanceEdit:3299684] May, B, 2013年04月20日
catalystActivity
[CatalystActivity:3299709] protein-disulfide reductase activity of CCS:Zn2+:2xCu1+:SOD1:Zn2+ [cytosol]
category
transition
compartment
[Compartment:70101] cytosol
created
[InstanceEdit:3299742] May, B, 2013年04月20日
dbId
3299753
displayName
CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1
edited
[InstanceEdit:3299684] May, B, 2013年04月20日
eventOf
[Pathway:R-HSA-3299685] Detoxification of Reactive Oxygen Species - Homo sapiens
followingEvent
[Reaction:R-HSA-3299691] SOD1 catalyzes 2H+ + 2O2.- => O2 + H2O2 (cytosol) - Homo sapiens
input
2 ×
[Complex:R-HSA-3299706] CCS:Zn2+:2xCu1+:SOD1:Zn2+ [cytosol]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:3299723] Human superoxide dismutase 1 (hSOD1) maturation through interaction with human copper chaperone for SOD1 (hCCS)
[LiteratureReference:3299724] The copper chaperone CCS directly interacts with copper/zinc superoxide dismutase
[LiteratureReference:3299740] The copper chaperone for superoxide dismutase
[LiteratureReference:3299746] Mechanism of Cu,Zn-superoxide dismutase activation by the human metallochaperone hCCS
[LiteratureReference:3299710] Oxygen and the copper chaperone CCS regulate posttranslational activation of Cu,Zn superoxide dismutase
[LiteratureReference:3299738] The effects of glutaredoxin and copper activation pathways on the disulfide and stability of Cu,Zn superoxide dismutase
[LiteratureReference:3299735] Different regulation of wild-type and mutant Cu,Zn superoxide dismutase localization in mammalian mitochondria
[LiteratureReference:3343746] Activation of Cu,Zn-superoxide dismutase in the absence of oxygen and the copper chaperone CCS
maxDepth
1
modified
[InstanceEdit:11033291] Weiser, Joel, 2025年08月28日
name
CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1
orthologousEvent
[Reaction:R-HSA-3780979] CCS transfers Cu to SOD1 (mitochondrial) - Homo sapiens
[Reaction:R-SCE-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Saccharomyces cerevisiae
[Reaction:R-DDI-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Dictyostelium discoideum
[Reaction:R-DME-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Drosophila melanogaster
[Reaction:R-GGA-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Gallus gallus
[Reaction:R-XTR-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Xenopus tropicalis
[Reaction:R-SSC-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Sus scrofa
[Reaction:R-BTA-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Bos taurus
[Reaction:R-CFA-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Canis familiaris
[Reaction:R-RNO-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Rattus norvegicus
[Reaction:R-MMU-3299753] CCS transfers Cu to SOD1 and oxidizes cysteine residues in SOD1 - Mus musculus
output
[Complex:R-HSA-3299679] 2xHC-SOD1:Zn2+:Cu2+ dimer [cytosol]
[Complex:R-HSA-3299731] CCS:Zn2+:Cu1+ dimer [cytosol]
precedingEvent
[Reaction:R-HSA-8951723] 2xSOD1:CCS:Zn2+:2xCu1+ dimer dissociates - Homo sapiens
releaseDate
2013年12月04日
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:4837339] Kavdia, Mahendra, 2013年11月01日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-3299753
summation
[Summation:3343709] Copper chaperone of superoxide dismutase (CCS) transfers a c...
Referrals
(hasEvent)
[Pathway:R-HSA-3299685] Detoxification of Reactive Oxygen Species
(precedingEvent)
[Reaction:R-HSA-3299691] SOD1 catalyzes 2H+ + 2O2.- => O2 + H2O2 (cytosol)
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