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Schema
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Reaction
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Entries
2Fe-2S is inserted in UQCRFS1
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authored
[InstanceEdit:9866273] Stephan, Ralf, 2024年03月27日
catalystActivity
[CatalystActivity:9866276] iron chaperone activity of FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix]
category
transition
compartment
[Compartment:70616] mitochondrial inner membrane
[Compartment:5460] mitochondrial matrix
created
[InstanceEdit:9866277] Stephan, Ralf, 2024年03月27日
dbId
9866272
displayName
2Fe-2S is inserted in UQCRFS1
edited
[InstanceEdit:9910822] Stephan, Ralf, 2024年05月21日
eventOf
[Pathway:R-HSA-9865881] Complex III assembly - Homo sapiens
followingEvent
[Reaction:R-HSA-9866253] apo-UQCRFS1 binds LYRM7 - Homo sapiens
[Reaction:R-HSA-9866164] Late core complex dimer binds UQCR10, UQCR11, UQCRFS1. - Homo sapiens
input
[Complex:R-HSA-1362398] FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix]
[Complex:R-HSA-9866263] UQCRFS1(1-274):LYRM7 [mitochondrial matrix]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:9854980] A Single Adaptable Cochaperone-Scaffold Complex Delivers Nascent Iron-Sulfur Clusters to Mammalian Respiratory Chain Complexes I-III
[LiteratureReference:9866265] Mitochondrial complex III Rieske Fe-S protein processing and assembly
maxDepth
1
modified
[InstanceEdit:11033291] Weiser, Joel, 2025年08月28日
name
2Fe-2S is inserted in UQCRFS1
orthologousEvent
[Reaction:R-BTA-9866272] 2Fe-2S is inserted in UQCRFS1 - Bos taurus
[Reaction:R-SCE-9866272] 2Fe-2S is inserted in UQCRFS1 - Saccharomyces cerevisiae
[Reaction:R-SPO-9866272] 2Fe-2S is inserted in UQCRFS1 - Schizosaccharomyces pombe
[Reaction:R-DDI-9866272] 2Fe-2S is inserted in UQCRFS1 - Dictyostelium discoideum
[Reaction:R-DME-9866272] 2Fe-2S is inserted in UQCRFS1 - Drosophila melanogaster
[Reaction:R-GGA-9866272] 2Fe-2S is inserted in UQCRFS1 - Gallus gallus
[Reaction:R-SSC-9866272] 2Fe-2S is inserted in UQCRFS1 - Sus scrofa
[Reaction:R-CFA-9866272] 2Fe-2S is inserted in UQCRFS1 - Canis familiaris
[Reaction:R-RNO-9866272] 2Fe-2S is inserted in UQCRFS1 - Rattus norvegicus
[Reaction:R-MMU-9866272] 2Fe-2S is inserted in UQCRFS1 - Mus musculus
output
[Complex:R-HSA-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix]
[Complex:R-HSA-164304] holo-UQCRFS1(1-274) [mitochondrial inner membrane]
[EntityWithAccessionedSequence:R-HSA-9866252] LYRM7 [mitochondrial matrix]
precedingEvent
[Reaction:R-HSA-9866253] apo-UQCRFS1 binds LYRM7 - Homo sapiens
previousReviewStatus
[ReviewStatus:9821383] three stars
regulatedBy
[Requirement:9866278] Requirement by 'HSPA9:HSCB [mitochondrial matrix]'
regulationReference
[RegulationReference:9866274] Requirement by 'HSPA9:HSCB [mitochondrial matrix]' A Single Adaptable Cochaperone-Scaffold Complex Delivers Nascent Iron-Sulfur Clusters to Mammalian Respiratory Chain Complexes I-III
releaseDate
2024年06月15日
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:9910688] Hill, David P, 2024年05月16日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-9866272
summation
[Summation:9866279] Frataxin (FXN) subunit of the 2Fe-2S transfer complex cataly...
Referrals
(hasEvent)
[Pathway:R-HSA-9865881] Complex III assembly
(precedingEvent)
[Reaction:R-HSA-9866164] Late core complex dimer binds UQCR10, UQCR11, UQCRFS1.
[Reaction:R-HSA-9866253] apo-UQCRFS1 binds LYRM7
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