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Schema
>
Complex
>
Entries
FXN:ISD11:NFS1:ISCU [mitochondrial matrix]
Show undefined attributes
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catalystActivities
[CatalystActivity:9954151] ferrous iron binding activity of FXN:ISD11:NFS1:ISCU [mitochondrial matrix]
compartment
[Compartment:5460] mitochondrial matrix
consumedByEvent
[Reaction:R-HSA-1362416] Frataxin binds iron - Homo sapiens
created
[InstanceEdit:1362403] May, B, 2011年06月09日
dbId
1362404
displayName
FXN:ISD11:NFS1:ISCU [mitochondrial matrix]
hasComponent
2 ×
[EntityWithAccessionedSequence:R-HSA-1362390] FXN(81-210) [mitochondrial matrix]
2 ×
[EntityWithAccessionedSequence:R-HSA-1362391] ISCU-1 [mitochondrial matrix]
2 ×
[EntityWithAccessionedSequence:R-HSA-1362392] LYRM4 [mitochondrial matrix]
2 ×
[EntityWithAccessionedSequence:R-HSA-1362396] PXLP-K258-NFS1-1 [mitochondrial matrix]
inDisease
false
inferredTo
[Complex:R-MMU-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Mus musculus
[Complex:R-RNO-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Rattus norvegicus
[Complex:R-CFA-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Canis familiaris
[Complex:R-BTA-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Bos taurus
[Complex:R-SSC-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Sus scrofa
[Complex:R-DRE-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Danio rerio
[Complex:R-XTR-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Xenopus tropicalis
[Complex:R-GGA-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Gallus gallus
[Complex:R-DME-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Drosophila melanogaster
[Complex:R-CEL-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Caenorhabditis elegans
[Complex:R-DDI-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Dictyostelium discoideum
[Complex:R-SPO-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Schizosaccharomyces pombe
[Complex:R-SCE-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Saccharomyces cerevisiae
[Complex:R-PFA-1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - Plasmodium falciparum
isChimeric
false
literatureReference
[LiteratureReference:1362328] Mammalian frataxin: an essential function for cellular viability through an interaction with a preformed ISCU/NFS1/ISD11 iron-sulfur assembly complex
[LiteratureReference:1362364] Human frataxin is an allosteric switch that activates the Fe-S cluster biosynthetic complex
[LiteratureReference:1362327] Mitochondrial frataxin interacts with ISD11 of the NFS1/ISCU complex and multiple mitochondrial chaperones
[LiteratureReference:1362323] Distinct iron-sulfur cluster assembly complexes exist in the cytosol and mitochondria of human cells
maxDepth
2
modified
[InstanceEdit:9644724] D'Eustachio, Peter, 2019年04月17日
name
FXN:ISD11:NFS1:ISCU
producedByEvent
[Reaction:R-HSA-9866272] 2Fe-2S is inserted in UQCRFS1 - Homo sapiens
[BlackBoxEvent:R-HSA-9854984] Transfer of Fe-S clusters to SDHB - Homo sapiens
schemaClass
Complex
species
[Species:48887] Homo sapiens
stId
R-HSA-1362404
updateTrackers
[UpdateTracker:9900538] Update Tracker - [Complex:1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - v69:[add_removeHasComponent]
Referrals
(updatedInstance)
[UpdateTracker:9900538] Update Tracker - [Complex:1362404] FXN:ISD11:NFS1:ISCU [mitochondrial matrix] - v69:[add_removeHasComponent]
(output)
[Reaction:R-HSA-9866272] 2Fe-2S is inserted in UQCRFS1
[BlackBoxEvent:R-HSA-9854984] Transfer of Fe-S clusters to SDHB
(input)
[Reaction:R-HSA-1362416] Frataxin binds iron
(physicalEntity)
[CatalystActivity:9954151] ferrous iron binding activity of FXN:ISD11:NFS1:ISCU [mitochondrial matrix]
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