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Schema
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Reaction
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Entries
Frataxin transfers Fe2+ to ACO2
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authored
[InstanceEdit:9854370] Stephan, Ralf, 2023年11月26日
catalystActivity
[CatalystActivity:9855646] iron chaperone activity of 2 Iron:FXN [mitochondrial matrix]
category
transition
compartment
[Compartment:5460] mitochondrial matrix
created
[InstanceEdit:9854399] Stephan, Ralf, 2023年11月26日
dbId
9854405
displayName
Frataxin transfers Fe2+ to ACO2
edited
[InstanceEdit:9861216] D'Eustachio, Peter, 2024年02月15日
eventOf
[Pathway:R-HSA-9854311] Maturation of TCA enzymes and regulation of TCA cycle - Homo sapiens
input
[Complex:R-HSA-1362402] 2 Iron:FXN [mitochondrial matrix]
[Complex:R-HSA-9854373] ACO2:3Fe-4S [mitochondrial matrix]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:9854395] Redox sensitive human mitochondrial aconitase and its interaction with frataxin: In vitro and in silico studies confirm that it takes two to tango
[LiteratureReference:9854392] Frataxin acts as an iron chaperone protein to modulate mitochondrial aconitase activity
[LiteratureReference:9854704] Friedreich's ataxia: point mutations and clinical presentation of compound heterozygotes
maxDepth
1
modified
[InstanceEdit:11033291] Weiser, Joel, 2025年08月28日
name
Frataxin transfers Fe2+ to ACO2
orthologousEvent
[Reaction:R-SCE-9854405] Frataxin transfers Fe2+ to ACO2 - Saccharomyces cerevisiae
[Reaction:R-SPO-9854405] Frataxin transfers Fe2+ to ACO2 - Schizosaccharomyces pombe
[Reaction:R-DDI-9854405] Frataxin transfers Fe2+ to ACO2 - Dictyostelium discoideum
[Reaction:R-CEL-9854405] Frataxin transfers Fe2+ to ACO2 - Caenorhabditis elegans
[Reaction:R-DME-9854405] Frataxin transfers Fe2+ to ACO2 - Drosophila melanogaster
[Reaction:R-GGA-9854405] Frataxin transfers Fe2+ to ACO2 - Gallus gallus
[Reaction:R-DRE-9854405] Frataxin transfers Fe2+ to ACO2 - Danio rerio
[Reaction:R-SSC-9854405] Frataxin transfers Fe2+ to ACO2 - Sus scrofa
[Reaction:R-BTA-9854405] Frataxin transfers Fe2+ to ACO2 - Bos taurus
[Reaction:R-CFA-9854405] Frataxin transfers Fe2+ to ACO2 - Canis familiaris
[Reaction:R-RNO-9854405] Frataxin transfers Fe2+ to ACO2 - Rattus norvegicus
[Reaction:R-MMU-9854405] Frataxin transfers Fe2+ to ACO2 - Mus musculus
output
[Complex:R-HSA-9854344] ACO2:4Fe-4S [mitochondrial matrix]
[SimpleEntity:R-ALL-113531] Fe2+ [mitochondrial matrix]
[EntityWithAccessionedSequence:R-HSA-1362390] FXN(81-210) [mitochondrial matrix]
precedingEvent
[Reaction:R-HSA-9854368] ROS,RNS oxidize ACO2:4Fe-4S - Homo sapiens
previousReviewStatus
[ReviewStatus:9821383] three stars
releaseDate
2024年03月27日
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:9861215] Hill, David P, 2024年02月15日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-9854405
summation
[Summation:9854393] Frataxin (FXN) is an iron chaperone that acts as a protein p...
Referrals
(hasEvent)
[Pathway:R-HSA-9854311] Maturation of TCA enzymes and regulation of TCA cycle
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