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Entries
GPIHBP1 binds HSPG:LPL dimer
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authored
[InstanceEdit:8857929] Jassal, Bijay, 2016年02月17日
category
binding
compartment
[Compartment:876] plasma membrane
[Compartment:984] extracellular region
created
[InstanceEdit:8857929] Jassal, Bijay, 2016年02月17日
dbId
8857928
displayName
GPIHBP1 binds HSPG:LPL dimer
edited
[InstanceEdit:8857929] Jassal, Bijay, 2016年02月17日
eventOf
[Pathway:R-HSA-8963889] Assembly of active LPL and LIPC lipase complexes - Homo sapiens
followingEvent
[Reaction:R-HSA-174757] chylomicron => TG-depleted chylomicron + 50 long-chain fatty acids + 50 diacylglycerols - Homo sapiens
input
[EntityWithAccessionedSequence:R-HSA-5216067] GPIHBP1 [plasma membrane]
[Complex:R-HSA-8867477] HSPG:LPL dimer [plasma membrane]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:8857959] Normal binding of lipoprotein lipase, chylomicrons, and apo-AV to GPIHBP1 containing a G56R amino acid substitution
[LiteratureReference:8857965] GPIHBP1, an endothelial cell transporter for lipoprotein lipase
[LiteratureReference:8857957] Glycosylphosphatidylinositol-anchored high-density lipoprotein-binding protein 1 and the intravascular processing of triglyceride-rich lipoproteins
[LiteratureReference:8857976] Homozygous missense mutation (G56R) in glycosylphosphatidylinositol-anchored high-density lipoprotein-binding protein 1 (GPI-HBP1) in two siblings with fasting chylomicronemia (MIM 144650)
[LiteratureReference:8857977] Chylomicronemia with a mutant GPIHBP1 (Q115P) that cannot bind lipoprotein lipase
[LiteratureReference:8857980] GPIHBP1 missense mutations often cause multimerization of GPIHBP1 and thereby prevent lipoprotein lipase binding
maxDepth
1
modified
[InstanceEdit:10778922] Weiser, Joel, 2025年08月27日
name
GPIHBP1 binds HSPG:LPL dimer
orthologousEvent
[Reaction:R-DME-8857928] GPIHBP1 binds HSPG:LPL dimer - Drosophila melanogaster
[Reaction:R-GGA-8857928] GPIHBP1 binds HSPG:LPL dimer - Gallus gallus
[Reaction:R-SSC-8857928] GPIHBP1 binds HSPG:LPL dimer - Sus scrofa
[Reaction:R-BTA-8857928] GPIHBP1 binds HSPG:LPL dimer - Bos taurus
[Reaction:R-CFA-8857928] GPIHBP1 binds HSPG:LPL dimer - Canis familiaris
[Reaction:R-RNO-8857928] GPIHBP1 binds HSPG:LPL dimer - Rattus norvegicus
[Reaction:R-MMU-8857928] GPIHBP1 binds HSPG:LPL dimer - Mus musculus
output
[Complex:R-HSA-8857969] GPIHBP1:HSPG:LPL dimer [plasma membrane]
precedingEvent
[Reaction:R-HSA-6784861] HSPG binds LPL dimer - Homo sapiens
releaseDate
2016年06月15日
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:8866933] D'Eustachio, Peter, 2016年04月05日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-8857928
summation
[Summation:8857975] Lipoprotein lipase (LPL) is mainly produced by adipocytes an...
Referrals
(hasEvent)
[Pathway:R-HSA-8963889] Assembly of active LPL and LIPC lipase complexes
(precedingEvent)
[Reaction:R-HSA-174757] chylomicron => TG-depleted chylomicron + 50 long-chain fatty acids + 50 diacylglycerols
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