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Schema
>
Reaction
>
Entries
guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine
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catalystActivity
[CatalystActivity:71283] methyltransferase activity of GAMT [cytosol]
category
transition
compartment
[Compartment:70101] cytosol
crossReference
[DatabaseIdentifier:12611068] Rhea:10657
dbId
71286
displayName
guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine
eventOf
[Pathway:R-HSA-71288] Creatine metabolism - Homo sapiens
followingEvent
[Reaction:R-HSA-200318] creatine + ATP => phosphocreatine + ADP [CKB,CKM] - Homo sapiens
[Reaction:R-HSA-200326] creatine + ATP => phosphocreatine + ADP [CK octamer] - Homo sapiens
input
[SimpleEntity:R-ALL-71284] AdoMet [cytosol]
[SimpleEntity:R-ALL-30401] GAA [cytosol]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:71277] Guanidinoacetate methyltransferase deficiency: the first inborn error of creatine metabolism in man.
maxDepth
1
modified
[InstanceEdit:11033291] Weiser, Joel, 2025年08月28日
name
guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine
orthologousEvent
[Reaction:R-SSC-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Sus scrofa
[Reaction:R-SCE-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Saccharomyces cerevisiae
[Reaction:R-SPO-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Schizosaccharomyces pombe
[Reaction:R-GGA-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Gallus gallus
[Reaction:R-XTR-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Xenopus tropicalis
[Reaction:R-DRE-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Danio rerio
[Reaction:R-BTA-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Bos taurus
[Reaction:R-CFA-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Canis familiaris
[Reaction:R-RNO-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Rattus norvegicus
[Reaction:R-MMU-71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - Mus musculus
output
[SimpleEntity:R-ALL-71285] AdoHcy [cytosol]
[SimpleEntity:R-ALL-29916] CRET [cytosol]
[SimpleEntity:R-ALL-70106] H+ [cytosol]
precedingEvent
[Reaction:R-HSA-71275] arginine + glycine => ornithine + guanidoacetate - Homo sapiens
releaseDate
2004年07月06日
reviewStatus
[ReviewStatus:9821382] five stars
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-71286
summation
[Summation:178831] Cytosolic guanidinoacetate methyltransferase catalyzes the r...
updateTrackers
[UpdateTracker:9792243] Update Tracker - [Reaction:71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - v22:[modifyText]
[UpdateTracker:9790716] Update Tracker - [Reaction:71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - v33:[addOutput]
Referrals
(updatedInstance)
[UpdateTracker:9792243] Update Tracker - [Reaction:71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - v22:[modifyText]
[UpdateTracker:9790716] Update Tracker - [Reaction:71286] guanidinoacetate + S-adenosylmethionine => creatine + S-adenosylhomocysteine - v33:[addOutput]
(hasEvent)
[Pathway:R-HSA-71288] Creatine metabolism
(precedingEvent)
[Reaction:R-HSA-200318] creatine + ATP => phosphocreatine + ADP [CKB,CKM]
[Reaction:R-HSA-200326] creatine + ATP => phosphocreatine + ADP [CK octamer]
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