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Schema
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Reaction
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Entries
ALDH9A1 tetramer dehydrogenates TEABL to form TEABT
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catalystActivity
[CatalystActivity:71259] 4-trimethylammoniobutyraldehyde dehydrogenase activity of ALDH9A1 tetramer [cytosol]
catalystActivityReference
[CatalystActivityReference:9643469] 4-trimethylammoniobutyraldehyde dehydrogenase activity of ALDH9A1 tetramer [cytosol] Kinetic and structural analysis of human ALDH9A1
category
transition
compartment
[Compartment:70101] cytosol
crossReference
[DatabaseIdentifier:12610794] Rhea:17986
dbId
71260
displayName
ALDH9A1 tetramer dehydrogenates TEABL to form TEABT
eventOf
[Pathway:R-HSA-71262] Carnitine synthesis - Homo sapiens
followingEvent
[Reaction:R-HSA-71261] BBOX1:AscH-:Fe2+ dimer dioxygenates TEABT and 2OG to form CAR and SUCCA - Homo sapiens
input
[SimpleEntity:R-ALL-29356] H2O [cytosol]
[SimpleEntity:R-ALL-29360] NAD+ [cytosol]
[SimpleEntity:R-ALL-31311] TEABL [cytosol]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:9794602] Kinetic and structural analysis of human ALDH9A1
[LiteratureReference:71252] Human aldehyde dehydrogenase. Purification and characterization of a third isozyme with low Km for gamma-aminobutyraldehyde
[LiteratureReference:71255] Molecular and biochemical characterization of rat gamma-trimethylaminobutyraldehyde dehydrogenase and evidence for the involvement of human aldehyde dehydrogenase 9 in carnitine biosynthesis.
maxDepth
1
modified
[InstanceEdit:10867632] Weiser, Joel, 2025年08月27日
name
ALDH9A1 tetramer dehydrogenates TEABL to form TEABT
4-(trimethylamino)butanal + H2O + NAD(+) => 4-(trimethylamino)butanoate + 2 H(+) + NADH
gamma-butyrobetaine semialdehyde + NAD+ => gamma-butyrobetaine + NADH + H+
orthologousEvent
[Reaction:R-CEL-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Caenorhabditis elegans
[Reaction:R-GGA-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Gallus gallus
[Reaction:R-XTR-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Xenopus tropicalis
[Reaction:R-DRE-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Danio rerio
[Reaction:R-SSC-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Sus scrofa
[Reaction:R-BTA-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Bos taurus
[Reaction:R-CFA-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Canis familiaris
[Reaction:R-RNO-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Rattus norvegicus
[Reaction:R-MMU-71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - Mus musculus
output
2 ×
[SimpleEntity:R-ALL-70106] H+ [cytosol]
[SimpleEntity:R-ALL-73473] NADH [cytosol]
[SimpleEntity:R-ALL-31369] TEABT [cytosol]
precedingEvent
[Reaction:R-HSA-71249] SHMT1 tetramer cleaves HTMLYS to yield TEABL and Gly - Homo sapiens
releaseDate
2004年07月06日
reviewStatus
[ReviewStatus:9821382] five stars
revised
[InstanceEdit:9794704] D'Eustachio, Peter, 2022年07月19日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-71260
summation
[Summation:178802] Cytosolic 4-trimethylaminobutyraldehyde dehydrogenase (ALDH9...
updateTrackers
[UpdateTracker:9790762] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v33:[addInput]
[UpdateTracker:9781553] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v60:[modifyText]
[UpdateTracker:9789375] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v38:[modifyText]
[UpdateTracker:9847012] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v82:[addLiteratureReference, modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9790762] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v33:[addInput]
[UpdateTracker:9781553] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v60:[modifyText]
[UpdateTracker:9789375] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v38:[modifyText]
[UpdateTracker:9847012] Update Tracker - [Reaction:71260] ALDH9A1 tetramer dehydrogenates TEABL to form TEABT - v82:[addLiteratureReference, modifyText]
(hasEvent)
[Pathway:R-HSA-71262] Carnitine synthesis
(precedingEvent)
[Reaction:R-HSA-71261] BBOX1:AscH-:Fe2+ dimer dioxygenates TEABT and 2OG to form CAR and SUCCA
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