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Schema
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Reaction
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Entries
POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653)
Show undefined attributes
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authored
[InstanceEdit:5615549] Jassal, Bijay, 2014年07月25日
catalystActivity
[CatalystActivity:5615563] dolichyl-phosphate-mannose-protein mannosyltransferase activity of POMT1:POMT2 [endoplasmic reticulum membrane]
category
transition
compartment
[Compartment:12045] endoplasmic reticulum membrane
[Compartment:17957] endoplasmic reticulum lumen
created
[InstanceEdit:5615549] Jassal, Bijay, 2014年07月25日
crossReference
[DatabaseIdentifier:9940846] RHEA:53397
dbId
5615637
displayName
POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653)
edited
[InstanceEdit:5615549] Jassal, Bijay, 2014年07月25日
eventOf
[Pathway:R-HSA-8932506] DAG1 core M1 glycosylations - Homo sapiens
followingEvent
[Reaction:R-HSA-9940735] FKTN transfers RboP to GalNAc-GlcNAc-ManP-DAG1 - Homo sapiens
[Reaction:R-HSA-8879117] POMGNT2 transfers GlcNAc to Man-DAG1 - Homo sapiens
goBiologicalProcess
[GO_BiologicalProcess:162021] protein O-linked glycosylation via mannose
input
[EntityWithAccessionedSequence:R-HSA-8931890] DAG1(30-653) [endoplasmic reticulum lumen]
3 ×
[SimpleEntity:R-ALL-449229] DOLP-Man [lumenal side of endoplasmic reticulum membrane]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:5615579] Demonstration of mammalian protein O-mannosyltransferase activity: coexpression of POMT1 and POMT2 required for enzymatic activity
[LiteratureReference:5615588] Congenital muscular dystrophies: a brief review
[LiteratureReference:5615623] The o-mannosylation pathway: glycosyltransferases and proteins implicated in congenital muscular dystrophy
[LiteratureReference:5615607] Mutations in the O-mannosyltransferase gene POMT1 give rise to the severe neuronal migration disorder Walker-Warburg syndrome
[LiteratureReference:9940716] The expanding phenotype of POMT1 mutations: from Walker-Warburg syndrome to congenital muscular dystrophy, microcephaly, and mental retardation
[LiteratureReference:9940658] An autosomal recessive limb girdle muscular dystrophy (LGMD2) with mild mental retardation is allelic to Walker-Warburg syndrome (WWS) caused by a mutation in the POMT1 gene
maxDepth
1
modified
[InstanceEdit:10778922] Weiser, Joel, 2025年08月27日
name
POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653)
orthologousEvent
[Reaction:R-DME-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Drosophila melanogaster
[Reaction:R-GGA-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Gallus gallus
[Reaction:R-XTR-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Xenopus tropicalis
[Reaction:R-DRE-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Danio rerio
[Reaction:R-SSC-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Sus scrofa
[Reaction:R-BTA-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Bos taurus
[Reaction:R-CFA-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Canis familiaris
[Reaction:R-RNO-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Rattus norvegicus
[Reaction:R-MMU-5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - Mus musculus
output
3 ×
[SimpleEntity:R-ALL-449311] DOLP [lumenal side of endoplasmic reticulum membrane]
3 ×
[SimpleEntity:R-ALL-156540] H+ [endoplasmic reticulum lumen]
[EntityWithAccessionedSequence:R-HSA-5615647] Man-DAG1 [endoplasmic reticulum lumen]
precedingEvent
[Reaction:R-HSA-9913329] Autoproteolysis of DAG1 to alpha and beta chains - Homo sapiens
[Reaction:R-HSA-162715] Reorientation of dolichyl phosphate D-mannose in the endoplasmic reticulum membrane - Homo sapiens
previousReviewStatus
[ReviewStatus:9821384] two stars
releaseDate
2016年03月23日
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:8849944] Hansen, Lars, Joshi, Hiren, 2015年12月18日
[InstanceEdit:9944933] D'Eustachio, Peter, 2025年04月08日
[InstanceEdit:9947107] Zaru, Rossana, 2025年05月01日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-5615637
summation
[Summation:5615592] Co-expression of both protein O-mannosyl-transferases 1 and ...
updateTrackers
[UpdateTracker:9953631] Update Tracker - [Reaction:5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - v93:[modifyText, removeLiteratureReference, removeOutput]
[UpdateTracker:9782766] Update Tracker - [Reaction:5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - v58:[add_removeInput, add_removeOutput, modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9953631] Update Tracker - [Reaction:5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - v93:[modifyText, removeLiteratureReference, removeOutput]
[UpdateTracker:9782766] Update Tracker - [Reaction:5615637] POMT1:POMT2 transfers Man from Dol-P-Man to DAG1(30-653) - v58:[add_removeInput, add_removeOutput, modifyText]
(normalReaction)
[FailedReaction:R-HSA-5615604] Defective POMT1 does not transfer Man from Dol-P-Man to DAG1
[FailedReaction:R-HSA-5615556] Defective POMT2 does not transfer Man from Dol-P-Man to DAG1
(precedingEvent)
[Reaction:R-HSA-9940735] FKTN transfers RboP to GalNAc-GlcNAc-ManP-DAG1
[Reaction:R-HSA-8879117] POMGNT2 transfers GlcNAc to Man-DAG1
(hasEvent)
[Pathway:R-HSA-8932506] DAG1 core M1 glycosylations
[Pathway:R-HSA-8932505] DAG1 core M3 glycosylations
[Pathway:R-HSA-8932504] DAG1 core M2 glycosylations
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