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Schema
>
Reaction
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Entries
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+
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authored
[InstanceEdit:517475] D'Eustachio, P, 2010年02月18日
catalystActivity
[CatalystActivity:70884] 3-hydroxyisobutyrate dehydrogenase activity of HIBADH tetramer [mitochondrial matrix]
category
transition
compartment
[Compartment:5460] mitochondrial matrix
created
[InstanceEdit:508464] D'Eustachio, P, 2010年02月12日
crossReference
[DatabaseIdentifier:12610558] Rhea:31277
[DatabaseIdentifier:9925945] RHEA:31277
dbId
508473
displayName
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+
edited
[InstanceEdit:517475] D'Eustachio, P, 2010年02月18日
eventOf
[Pathway:R-HSA-70895] Branched-chain amino acid catabolism - Homo sapiens
input
[SimpleEntity:R-ALL-30004] 2M3OPROA [mitochondrial matrix]
[SimpleEntity:R-ALL-113529] H+ [mitochondrial matrix]
[SimpleEntity:R-ALL-29362] NADH [mitochondrial matrix]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:70886] Purification and properties of beta-hydroxyisobutyric dehydrogenase
maxDepth
1
modified
[InstanceEdit:10948619] Weiser, Joel, 2025年08月27日
name
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+
(S)-2-methyl-3-oxopropanoate + H(+) + NADH => (S)-3-hydroxy-2-methylpropanoate + NAD(+)
negativePrecedingEvent
[NegativePrecedingEvent:9908865] Futile Cycle: beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+
orthologousEvent
[Reaction:R-DDI-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Dictyostelium discoideum
[Reaction:R-CEL-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Caenorhabditis elegans
[Reaction:R-DME-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Drosophila melanogaster
[Reaction:R-GGA-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Gallus gallus
[Reaction:R-XTR-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Xenopus tropicalis
[Reaction:R-DRE-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Danio rerio
[Reaction:R-SSC-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Sus scrofa
[Reaction:R-BTA-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Bos taurus
[Reaction:R-CFA-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Canis familiaris
[Reaction:R-RNO-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Rattus norvegicus
[Reaction:R-MMU-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Mus musculus
output
[SimpleEntity:R-ALL-573404] bHIBA [mitochondrial matrix]
[SimpleEntity:R-ALL-113526] NAD+ [mitochondrial matrix]
releaseDate
2010年03月16日
reverseReaction
[Reaction:R-HSA-70885] beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:532425] Jassal, Bijay, 2010年02月26日
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-508473
summation
[Summation:508467] Mitochondrial 3-hydroxyisobutyrate dehydrogenase (HIBADH) ca...
updateTrackers
[UpdateTracker:9790479] Update Tracker - [Reaction:508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - v33:[add_removeOutput]
Referrals
(updatedInstance)
[UpdateTracker:9790479] Update Tracker - [Reaction:508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - v33:[add_removeOutput]
(hasEvent)
[Pathway:R-HSA-70895] Branched-chain amino acid catabolism
(precedingEvent)
[NegativePrecedingEvent:9908870] Futile Cycle: methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+
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