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Schema
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Reaction
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Entries
Reduction of desmosterol to cholesterol
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authored
[InstanceEdit:196418] D'Eustachio, P, 2007年04月21日 18:31:40
catalystActivity
[CatalystActivity:196404] Delta24-sterol reductase activity of DHCR24 [endoplasmic reticulum membrane]
catalystActivityReference
[CatalystActivityReference:9643615] delta24-sterol reductase activity of DHCR24 [endoplasmic reticulum membrane] Mutations in the 3beta-hydroxysterol Delta24-reductase gene cause desmosterolosis, an autosomal recessive disorder of cholesterol biosynthesis
category
transition
compartment
[Compartment:70101] cytosol
[Compartment:12045] endoplasmic reticulum membrane
created
[InstanceEdit:196422] D'Eustachio, P, 2007年04月21日 18:35:08
crossReference
[DatabaseIdentifier:12610970] Rhea:36391
[DatabaseIdentifier:9945225] RHEA:36393
dbId
196417
displayName
Reduction of desmosterol to cholesterol
edited
[InstanceEdit:196418] D'Eustachio, P, 2007年04月21日 18:31:40
eventOf
[Pathway:R-HSA-6807047] Cholesterol biosynthesis via desmosterol - Homo sapiens
followingEvent
[Reaction:R-HSA-5250531] ARV1 transports CHOL from ER membrane to plasma membrane - Homo sapiens
input
[SimpleEntity:R-ALL-196420] DESMOL [endoplasmic reticulum membrane]
[SimpleEntity:R-ALL-70106] H+ [cytosol]
[SimpleEntity:R-ALL-29364] NADPH [cytosol]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:196421] Mutations in the 3beta-hydroxysterol Delta24-reductase gene cause desmosterolosis, an autosomal recessive disorder of cholesterol biosynthesis
maxDepth
1
modified
[InstanceEdit:10867632] Weiser, Joel, 2025年08月27日
name
Reduction of desmosterol to cholesterol
desmosterol + NADPH + H(+) => cholesterol + NADP(+)
orthologousEvent
[Reaction:R-RNO-196417] Reduction of desmosterol to cholesterol - Rattus norvegicus
[Reaction:R-CEL-196417] Reduction of desmosterol to cholesterol - Caenorhabditis elegans
[Reaction:R-GGA-196417] Reduction of desmosterol to cholesterol - Gallus gallus
[Reaction:R-XTR-196417] Reduction of desmosterol to cholesterol - Xenopus tropicalis
[Reaction:R-DRE-196417] Reduction of desmosterol to cholesterol - Danio rerio
[Reaction:R-SSC-196417] Reduction of desmosterol to cholesterol - Sus scrofa
[Reaction:R-BTA-196417] Reduction of desmosterol to cholesterol - Bos taurus
[Reaction:R-CFA-196417] Reduction of desmosterol to cholesterol - Canis familiaris
[Reaction:R-MMU-196417] Reduction of desmosterol to cholesterol - Mus musculus
output
[SimpleEntity:R-ALL-193384] CHOL [endoplasmic reticulum membrane]
[SimpleEntity:R-ALL-29366] NADP+ [cytosol]
precedingEvent
[Reaction:R-HSA-196402] Cholesta-5,7,24-trien-3beta-ol is reduced to desmosterol - Homo sapiens
releaseDate
2007年02月20日
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:196409] Jassal, B, 2007年04月21日 18:33:24
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-196417
summation
[Summation:196412] Desmosterol is reduced by NADPH + H+ to form cholesterol and...
updateTrackers
[UpdateTracker:9791026] Update Tracker - [Reaction:196417] Reduction of desmosterol to cholesterol - v32:[addOutput]
Referrals
(updatedInstance)
[UpdateTracker:9791026] Update Tracker - [Reaction:196417] Reduction of desmosterol to cholesterol - v32:[addOutput]
(hasEvent)
[Pathway:R-HSA-6807047] Cholesterol biosynthesis via desmosterol
(precedingEvent)
[Reaction:R-HSA-5250531] ARV1 transports CHOL from ER membrane to plasma membrane
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