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Schema
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Reaction
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Entries
propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate
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catalystActivity
[CatalystActivity:71030] propionyl-CoA carboxylase activity of 6x(Btn-PCCA:PCCB) [mitochondrial matrix]
catalystActivityReference
[CatalystActivityReference:9643743] propionyl-CoA carboxylase activity of 6x(Btn-PCCA:PCCB) [mitochondrial matrix] Isolation and characterization of propionyl-CoA carboxylase from normal human liver. Evidence for a protomeric tetramer of nonidentical subunits
category
transition
compartment
[Compartment:5460] mitochondrial matrix
dbId
71031
displayName
propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate
eventOf
[Pathway:R-HSA-71032] Propionyl-CoA catabolism - Homo sapiens
followingEvent
[Reaction:R-HSA-71020] D-methylmalonyl-CoA <=> L-methylmalonyl-CoA - Homo sapiens
input
[SimpleEntity:R-ALL-113593] ATP [mitochondrial matrix]
[SimpleEntity:R-ALL-29376] CO2 [mitochondrial matrix]
[SimpleEntity:R-ALL-70843] PROP-CoA [mitochondrial matrix]
isInDisease
false
isInferred
false
literatureReference
[Book:71000] The Metabolic and Molecular Bases of Inherited Disease, 8th ed Scriver, CR Disorders of propionate and methylmalonate metabolism 0079130356
[LiteratureReference:449696] Isolation and characterization of propionyl-CoA carboxylase from normal human liver. Evidence for a protomeric tetramer of nonidentical subunits
[LiteratureReference:71027] Metabolism of propionic acid in animal tissues. VIII. Crystalline propionyl carboxylase
[LiteratureReference:1112677] Mitochondrial targeting signals and mature peptides of 3-methylcrotonyl-CoA carboxylase
maxDepth
1
modified
[InstanceEdit:10948619] Weiser, Joel, 2025年08月27日
name
propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate
orthologousEvent
[Reaction:R-DRE-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Danio rerio
[Reaction:R-DDI-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Dictyostelium discoideum
[Reaction:R-CEL-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Caenorhabditis elegans
[Reaction:R-GGA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Gallus gallus
[Reaction:R-XTR-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Xenopus tropicalis
[Reaction:R-SSC-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Sus scrofa
[Reaction:R-BTA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Bos taurus
[Reaction:R-CFA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Canis familiaris
[Reaction:R-RNO-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Rattus norvegicus
[Reaction:R-MMU-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Mus musculus
output
[SimpleEntity:R-ALL-113581] ADP [mitochondrial matrix]
[SimpleEntity:R-ALL-71019] MEMA-CoA [mitochondrial matrix]
[SimpleEntity:R-ALL-113548] Pi [mitochondrial matrix]
precedingEvent
[Reaction:R-HSA-70844] alpha-methylacetoacetyl-CoA + CoA => propionyl-CoA + acetyl-CoA - Homo sapiens
[Reaction:R-HSA-70893] methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ - Homo sapiens
releaseDate
2004年07月06日
reviewStatus
[ReviewStatus:9821382] five stars
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-71031
summation
[Summation:179123] Propionyl CoA carboxylase in the mitochondrial matrix cataly...
updateTrackers
[UpdateTracker:9790811] Update Tracker - [Reaction:71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - v32:[addLiteratureReference, modifyText]
[UpdateTracker:9789904] Update Tracker - [Reaction:71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - v36:[addLiteratureReference, modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9790811] Update Tracker - [Reaction:71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - v32:[addLiteratureReference, modifyText]
[UpdateTracker:9789904] Update Tracker - [Reaction:71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - v36:[addLiteratureReference, modifyText]
(hasEvent)
[Pathway:R-HSA-71032] Propionyl-CoA catabolism
(precedingEvent)
[Reaction:R-HSA-71020] D-methylmalonyl-CoA <=> L-methylmalonyl-CoA
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